FEVER, PANCYTOPENIA, HEMOPHAGOCYTOSIS—CLINICAL ANALYSIS OF A CASE OF HEMATOLOGICAL SYSTEM DISEASE WITH BONE MARROW FAILURE AS THE PROMINENT MANIFESTATION
Download as PDFVolume 2, Issue 1, Pp 13-16, 2019
Author(s)
Liu Xiaofang1, Liu Lei1*, Lei Anhui1, He Jun2, Guo Pengxiang2
Affiliation(s)
1Department of Hematology, The First People’s Hospital of Guiyang, 550002, Guiyang, China
2Department of Hematology, The People’s Hospital of Guizhou Province, 550002, Guiyang, China
Corresponding Author
Liu Lei
ABSTRACT
The object is to improve the recognition and differentiation of rare diseases of bone marrow failure. The method is to report a case with fever as the main symptom, pancytopenia, myelodysplasia and hemophagocytosis in the laboratory and to review literature. Results: The patient had fever for more than one month, no lymphadenopathy, but with hepatosplenomegaly, myelodysplasia with hemophagocytosis, EB virus infection. The hemogram recovered after 20 days of treatment. Conclusion: Hemophagocytic syndrome, acute aplastic crisis and severe aplastic anemia, the clinical manifestations can overlap. When the diagnosis is not very clear, the treatment should be based on strong supportive treatment, at the same time actively look for the causes, and remove the relevant factors.
KEYWORDS
fever; pancytopenia; hemophagocytic syndrome
CITE THIS PAPER
Liu Xiaofang, Liu Lei, Lei Anhui, He Jun, Guo Pengxiang. Fever, pancytopenia, hemophagocytosis—clinical analysis of a case of hematological system disease with bone marrow failure as the prominent manifestation. Acta Translational Medicine. 2019, 2(1): 13-16.
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